Prognostic Impact of Organomegaly in Mastocytosis: An Analysis of the European Competence Network on Mastocytosis

Authors

LUEBKE Johannes SCHWAAB Juliana CHRISTEN Deborah ELBERINK Hanneke Oude SPAN Bart NIEDOSZYTKO Marek GORSKA Aleksandra LANGE Magdalena GLEIXNER Karoline V HADZIJUSUFOVIC Emir SOLOMIANYI Oleksii ANGELOVA-FISCHER Irena ZANOTTI Roberta BONIFACIO Massimiliano BONADONNA Patrizia SHOUMARIYEH Khalid NIKOLAS von Bubnoff MUELLER Sabine PERKINS Cecelia ELENA Chiara MALCOVATI Luca HAGGLUND Hans MATTSSON Mattias PARENTE Roberta VARKONYI Judit FORTINA Anna Belloni CAROPPO Francesca ZINK Alexander BROCKOW Knut BREYNAERT Christine BULLENS Dominique YAVUZ Akif Selim DOUBEK Michael SABATO Vito SCHUG Tanja NIEDERWIESER Dietger HARTMANN Karin TRIGGIANI Massimo GOTLIB Jason HERMINE Olivier AROCK Michel KLUIN-NELEMANS Hanneke C PANSE Jens SPERR Wolfgang R VALENT Peter REITER Andreas JAWHAR Mohamad

Year of publication 2023
Type Article in Periodical
Magazine / Source JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY-IN PRACTICE
MU Faculty or unit

Faculty of Medicine

Citation
Web https://www.sciencedirect.com/science/article/abs/pii/S2213219822011977?via%3Dihub
Doi http://dx.doi.org/10.1016/j.jaip.2022.10.051
Keywords Mastocytosis; Systemic mastocytosis; Organomegaly; Splenomegaly; Hepatomegaly; Lymphadenopathy
Description BACKGROUND: Organomegaly, including splenomegaly, hepatomegaly, and/or lymphadenopathy, are important diagnostic and prognostic features in patients with cutaneous mastocytosis (CM) or systemic mastocytosis (SM).

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