Rare non-Hodgkin lymphoma of childhood and adolescence: A consensus diagnostic and therapeutic approach to pediatric-type follicular lymphoma, marginal zone lymphoma, and nonanaplastic peripheral T-cell lymphoma

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Publikace nespadá pod Lékařskou fakultu, ale pod Středoevropský technologický institut. Oficiální stránka publikace je na webu muni.cz.
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ATTARBASCHI A. ABLA O. PADILLA L.A. BEISHUIZEN A. BURKE G.A.A. BRUGIERES L. BRUNEAU J. BURKHARDT B. D AMORE E.S.G. KLAPPER W. KONTNY U. PILLON M. TAJ M. TURNER Suzanne Dawn UYTTEBROECK A. WOESSMANN W. MELLGREN K.

Rok publikování 2020
Druh Článek v odborném periodiku
Časopis / Zdroj PEDIATRIC BLOOD & CANCER
Fakulta / Pracoviště MU

Středoevropský technologický institut

Citace
www https://onlinelibrary.wiley.com/doi/full/10.1002/pbc.28416
Doi http://dx.doi.org/10.1002/pbc.28416
Klíčová slova follicular lymphoma; marginal zone lymphoma; non-Hodgkin lymphoma; peripheral T-cell lymphoma; rare
Popis Pediatric-type follicular (PTFL), marginal zone (MZL), and peripheral T-cell lymphoma (PTCL) account each for <2% of childhood non-Hodgkin lymphoma. We present clinical and histopathological features of PTFL, MZL, and few subtypes of PTCL and provide treatment recommendations. For localized PTFL and MZL, watchful waiting after complete resection is the therapy of choice. For PTCL, therapy is subtype-dependent and ranges from a block-like anaplastic large cell lymphoma (ALCL)-derived and, alternatively, leukemia-derived therapy in PTCL not otherwise specified and subcutaneous panniculitis-like T-cell lymphoma to a block-like mature B-NHL-derived or, preferentially, ALCL-derived treatment followed by hematopoietic stem cell transplantation in first remission in hepatosplenic and angioimmunoblastic T-cell lymphoma.

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