Rare syringoid eccrine carcinoma of the upper lip and nasal base treated with resection and subsequent innovative reconstruction using an Abbe flap, turbinate flaps and three-stage forehead flap: a case report



Rok publikování 2022
Druh Článek v odborném periodiku
Časopis / Zdroj World Journal of Surgical Oncology
Fakulta / Pracoviště MU

Lékařská fakulta

www https://wjso.biomedcentral.com/articles/10.1186/s12957-022-02754-4
Doi http://dx.doi.org/10.1186/s12957-022-02754-4
Klíčová slova Syringoid eccrine carcinoma; Head and neck malignancy; Nasal reconstruction; Turbinate flap; Functional endonasal surgery
Popis Background Although syringoma is a common benign tumour of the sudoriferous gland, there is also an extremely rare malignant form known as syringoid eccrine carcinoma (SEC). SEC usually exhibits slow growth with deep invasion and a frequent tendency to relapse. The treatment of choice is radical wide resection, which poses a difficult reconstructive problem, especially when the tumour is located in the centre of the face. Case presentation In this case, a 70-year-old man was diagnosed with an SEC at the same location as a benign syringoma of the upper lip and nasal base that had undergone primary excision 7 years prior. Primary radical resection was performed with immediate Abbe flap reconstruction. Nevertheless, histology revealed positive margins, and 3 additional re-excisions were needed to achieve clear margins. Four months after the initial resection, the patient had undergone an innovative reconstruction technique including not only the Abbe flap but also a turbinate flap harvested with functional endonasal surgery and a three-stage forehead flap. Conclusion To the best of our knowledge, this is the first case report of a suspect malignant transformation of a benign syringoma after 7 years. In addition, from oncoplastic and reconstructive points of view, the bilateral use of the turbinate flap for reconstructing the intranasal lining of the alar base is unusual, and the use of functional endonasal surgery in nasal reconstruction for reducing the risk of damaging the vascular supply of the flap is innovative.

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